Recurrent diffuse alveolar hemorrhage and extracorporeal membrane oxygenation utilization in a hematopoietic stem cell transplant patient with Hunters syndrome

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Published Apr 24, 2024
DOI: https://doi.org/10.22551/2024.42.1101.10281
Nasreen Noor Gene Peir Asdís Finnsdottir Wagner Jay Rilinger Jenna Miller

Abstract

We describe the natural history of a three-month-old patient with Hunter Syndrome with hematopoietic stem cell transplant (HSCT) who developed recurrent diffuse alveolar hemorrhage (DAH) requiring extracorporeal membrane oxygenation (ECMO). The patient underwent HSCT with several complications, including veno-occlusive disease and DAH. He was managed with ECMO. Unfortunately, despite initial success he developed recurrent DAH and ultimately died. This is a novel report of this severe adverse event requiring ECMO following the use of HSCT in this rare patient population. We share the clinical strategies employed to address the complications associated with HSCT and the progression of his disease over his hospitalization.

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Keywords

diffuse alveolar hemorrhage (DAH), extra corporal membrane oxygenation (ECMO), Hunters syndrome, bone marrow transplant, pulmonary hemorrhage

References
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How to Cite
Noor, N., Peir, G., Finnsdottir Wagner, A., Rilinger, J., & Miller, J. (2024). Recurrent diffuse alveolar hemorrhage and extracorporeal membrane oxygenation utilization in a hematopoietic stem cell transplant patient with Hunters syndrome. Archive of Clinical Cases, 11(1), 19-21. https://doi.org/10.22551/2024.42.1101.10281
Issue
Vol. 11 No. 1 (2024)
Section
Case Reports
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How to Cite

Noor, N., Peir, G., Finnsdottir Wagner, A., Rilinger, J., & Miller, J. (2024). Recurrent diffuse alveolar hemorrhage and extracorporeal membrane oxygenation utilization in a hematopoietic stem cell transplant patient with Hunters syndrome. Archive of Clinical Cases, 11(1), 19-21. https://doi.org/10.22551/2024.42.1101.10281