Calcifying nested stromal-epithelial tumor (CNSET) of the liver
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Abstract
Calcifying nested stromal-epithelial tumor (CNSET) of the liver is an extremely rare primary tumor of non-hepatic and non-biliary origins which generally affects children and young adults, mainly women. We report a case of 28-year-old woman with a history of oral contraceptive consumption for 9 years, who underwent surgery for a large right hepatic mass that proved to be a CNSET, according to the pathology report. Postoperatively the patient had a slow recovery and after discharge the patient was sent to the oncology department where she underwent several treatment cycles with Imatinib. The case report documented all the clinical and histopathological features necessary for diagnosis of CNSET. CNSET of liver should always be considered and included in the differential diagnosis of hepatic tumors especially if the patient is a young woman with a long history of oral contraceptive consumption and an abdominal palpable mass.
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calcifying nested stromal-epithelial tumor, hepatic tumor, hepatoblastoma, liver, mixed tumor
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